Entry - %602639 - TOOTH AGENESIS, SELECTIVE, 2; STHAG2 - OMIM - (MIRROR)
% 602639

TOOTH AGENESIS, SELECTIVE, 2; STHAG2


Alternative titles; symbols

HYPODONTIA/OLIGODONTIA 2; HYD2


HGNC Approved Gene Symbol: HYD2

Cytogenetic location: 16q12.1   Genomic coordinates (GRCh38) : 16:47,000,001-52,600,000


Gene-Phenotype Relationships
Location Phenotype Phenotype
MIM number
Inheritance Phenotype
mapping key
16q12.1 Tooth agenesis, selective, 2 602639 2
Phenotypic Series
 


TEXT

For a phenotypic description and a discussion of genetic heterogeneity of selective tooth agenesis, see STHAG1 (106600).


Clinical Features

Ahmad et al. (1998) described a consanguineous kindred in Pakistan segregating hypodontia associated with dental anomalies such as malformation, enamel hypoplasia, and failure of eruption, leading prematurely to the edentulous state.


Inheritance

The transmission pattern of hypodontia with other dental anomalies in the family reported by Ahmad et al. (1998) was consistent with autosomal recessive inheritance.


Mapping

In studies of a consanguineous kindred in Pakistan segregating hypodontia with various dental anomalies, Ahmad et al. (1998) demonstrated linkage of the trait to a 10-cM region on 16q12.1; maximum 2-point lod score = 5.76 for marker D16S3140.


REFERENCES

  1. Ahmad, W., Brancolini, V., Faiyaz ul Haque, M., Lam, H., ul Haque, S., Haider, M., Maimon, A., Aita, V. M., Owen, J., Brown, D., Zegarelli, D. J., Ahmad, M., Ott, J., Christiano, A. M. A locus for autosomal recessive hypodontia with associated dental anomalies maps to chromosome 16q12.1. (Letter) Am. J. Hum. Genet. 62: 987-991, 1998. [PubMed: 9529357, related citations] [Full Text]


Creation Date:
Victor A. McKusick : 5/20/1998
carol : 11/21/2017
alopez : 05/05/2010
carol : 4/5/2007
mgross : 3/18/2004
carol : 11/27/2000
alopez : 3/20/2000
alopez : 5/20/1998

% 602639

TOOTH AGENESIS, SELECTIVE, 2; STHAG2


Alternative titles; symbols

HYPODONTIA/OLIGODONTIA 2; HYD2


HGNC Approved Gene Symbol: HYD2

DO: 0050591;  


Cytogenetic location: 16q12.1   Genomic coordinates (GRCh38) : 16:47,000,001-52,600,000


Gene-Phenotype Relationships

Location Phenotype Phenotype
MIM number
Inheritance Phenotype
mapping key
16q12.1 Tooth agenesis, selective, 2 602639 2

TEXT

For a phenotypic description and a discussion of genetic heterogeneity of selective tooth agenesis, see STHAG1 (106600).


Clinical Features

Ahmad et al. (1998) described a consanguineous kindred in Pakistan segregating hypodontia associated with dental anomalies such as malformation, enamel hypoplasia, and failure of eruption, leading prematurely to the edentulous state.


Inheritance

The transmission pattern of hypodontia with other dental anomalies in the family reported by Ahmad et al. (1998) was consistent with autosomal recessive inheritance.


Mapping

In studies of a consanguineous kindred in Pakistan segregating hypodontia with various dental anomalies, Ahmad et al. (1998) demonstrated linkage of the trait to a 10-cM region on 16q12.1; maximum 2-point lod score = 5.76 for marker D16S3140.


REFERENCES

  1. Ahmad, W., Brancolini, V., Faiyaz ul Haque, M., Lam, H., ul Haque, S., Haider, M., Maimon, A., Aita, V. M., Owen, J., Brown, D., Zegarelli, D. J., Ahmad, M., Ott, J., Christiano, A. M. A locus for autosomal recessive hypodontia with associated dental anomalies maps to chromosome 16q12.1. (Letter) Am. J. Hum. Genet. 62: 987-991, 1998. [PubMed: 9529357] [Full Text: https://doi.org/10.1086/301799]


Creation Date:
Victor A. McKusick : 5/20/1998

Edit History:
carol : 11/21/2017
alopez : 05/05/2010
carol : 4/5/2007
mgross : 3/18/2004
carol : 11/27/2000
alopez : 3/20/2000
alopez : 5/20/1998